Posterior Kyphectomy in a Myelomeningocele Patient with Gibbus Deformity: A Case Report and Literature Review

Authors

1 Department of Neurosurgery, Faculty of Medicine, Mashhad University of Medical Sciences, Mashhad, Iran.

2 Department of Radiology, Faculty of Medicine, Mashhad University of Medical Sciences, Mashhad, Iran.

3 Functional Neurosurgery Research center , Shohada Tajrish Neurosurgical Comprehensive Center of Excellence , Shahid Beheshti University of Medical Sciences , Tehran , Iran.

10.22038/ijp.2020.48810.3920

Abstract

Myelomeningocle is a condition caused by disjunction of neurectoderm and ectoderm during embryogenesis. It can lead to neuronal structure disorders such as kyphosis and scoliosis. However scoliosis is more common in these patients. Kyphosis found in 10-15% of these patients and can cause poor clinical consequences. Kyphosis progression is reported about 8-12 degrees yearly.  Kyphosis is a limiting factor in rehabilitation of these patients due to inability sitting on wheelchair and superficial ulcers in apex of kyphotic region. Here we aimed to describe a similar case in a 14-years-old man who underwent surgery for posterior kyphectomy. In the majority of cases with kyphosis, anterior wedging occurs in the vertebral body where the apex of the deformity is located. In our patient deformity had a round curve with no definite apex that could be marked out. These deformities need special surgical approaches and postoperative care.

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