A Rare Case of Budd Chiari Syndrome in a Child

Authors

1 Professor, Department Of Pediatrics, Jawaharlal Nehru Medical College, Sawangi Meghe, Wardha, Maharashtra -4420004, India.

2 Associate Professor, Department Of Pediatrics, Jawaharlal Nehru Medical College, Sawangi Meghe, Wardha, Maharashtra -4420004, India.

3 Resident, Department Of Pediatrics, Jawaharlal Nehru Medical College, Sawangi Meghe, Wardha, Maharashtra -4420004, India.

4 Senior Resident, Department Of Pediatrics, Jawaharlal Nehru Medical College, Sawangi Meghe, Wardha, Maharashtra -4420004, India.

5 Interventional Radiologist, Department of Radiology, Jawaharlal Nehru Medical College, Sawangi Meghe, Wardha, Maharashtra -4420004, India.

Abstract

A 7-year- old male child presented with the complaints of tense abdominal distension and swelling over feet since 1 month. The patient had repeated episodes of similar complaints since last two years with partial or complete relief after taking various forms of allopathic therapy. On imaging, Budd-Chiari syndrome was diagnosed which was hallmarked by occluded Inferior venacava (IVC), caudate lobe enlargement and heterogeneous liver enhancement. Initially thrombolysis done leading to complete remission for the patient for 15 days, later on again the patient developed similar complaints for which balloon venoplasty and hepatic vein stenting was done.

Keywords