1 Department of Pediatric Surgery of Hazrat Masoume Hospital, Qom University of Medical Sciences, Qom, Iran.

2 School of Medicine, Qom University of Medical Sciences, Qom, Iran.


     Urethralduplication is a rare condition occurs as a congenital malformation either independently or in the setting of other congenital malformations such as caudal duplication syndrome. Its prevalence becomes even rarer if it manifests as two side-by-side tracts in coronal plan.
Nonetheless, we introduce a unique presentation of complete coronal urethral duplication accompanied by astounding manifestations of gastrointestinal malformations different from what is expected for a normal hind gut or caudal duplication syndrome. A 6-year-old boy with complete coronal duplication of urethra along with duplication of appendix, sigmoid and rectum as well as developmental delay, attracted our attention to report.